EzempiloIzifo Nezimo

Okuncane mayelana nokuthi yi-hemophilia

I-Hemophilia yisifo esibi nesidumile. Labo abanesithakazelo emlandweni bayazi ukuthi lesi sifo sabhekana nendodana yezokugcina yaseRussia uTar Nicholas II - Alexei. Kodwa yini i-hemophilia futhi iyadluliselwa kanjani?

I-Hemophilia yisifo esiwufa esihlotshaniswa ne-blood clotting disorder, ngenxa yokuthi umuntu angafa ngisho nangenxa yokulimala okuncane noma ukulimala, lapho umuntu onempilo engeke akwazi ukulalela. Akunakwenzeka ukuba umuntu athole i-hemophilia, ngoba imbangela yaso yisici se-genetic defect defect. Kunezinhlobo ezintathu zezifo, okungafani nokuphulwa kwezici ezithile ze-coagulation. Abesifazane ngokwabo abafuni neze ukuthola i-hemophilia, kodwa bayithwala lesi sifo sofuzo futhi bangakwazi ukubeletha izingane ezizohlolwa nge-hemophilia. Emadodeni, ngokuvamile kuvunyelwe esemncane esebenzisa ukuhlolwa kwegazi.

Ukuphulukisa i-hemophilia engakafundiwe ngokugcwele, kepha iziguli zithola izijoka ezidingekayo futhi azikwazi ukwesaba ukuphuma kwangaphakathi. Noma kunjalo, kufanele bahlale beqaphe futhi baqaphele ukulimala. Lesi sifo sibonakala kusukela esemncane futhi singatholakala ngisho nasesibhedlela ngisho nangesikhathi sokukhulelwa. Izimpawu eziyinhloko ze-hemophilia yilezi: ukuphuma kwegazi, ukuvuthwa emva kokuvuthwa, ukuphuma kwegazi emva kokungenelela okuncane okuhlinzekwa ukuhlinzwa.

Ngokusho kwe-WHO, kunezinkulungwane ezingu-400 zabantu ababhekene ne-hemophilia emhlabeni. Ngo-1989, usuku lwasungulwa ukulwa nalesi sifo esiyingozi, esenzelwe ukudweba abantu ngale nkinga, ukuze bacabange ukuthi i-hemophilia yiyiphi, izinga lokuphila kulabo ababulawa ngisho nokubulawa kwesinyo.

Ngaphandle kwezinhlobo zezifo, i-hemophilia nayo ihlukahluka ngokweqile, Kuye ngesilinganiso sokuntuleka kwalokhu noma leso sici segazi coagulation. Iyini i-hemophilia ngesimo esincane? Ngakho-ke kuthiwa yi-degree yesifo, lapho ukuphuma kwegazi kuqala kuphela ngemva kokubi kakhulu Ukungenelela nokulimala. Ifomu elilinganiselwe lingafundwa esikoleni sasenkulisa noma esikoleni, sibonakala ekubukeni kwemivimbo emikhulu emva kokuvuthwa okuncane. Ifomu elibi liphuma ezinsaneni ngesikhathi sezinyosi kanye ne-hemomas enkulu, ngokushesha nje lapho ingane ifunda ukuhamba ngokuzimela: khaza bese uhamba.

Ngaphandle kokuthi labo abazi ukuthi i-hemophilia bayibona yini, badinga usizo lwezokwelapha mayelana nokulimala, bona, kanye nezihlobo zabo, badinga ukusekelwa kwengqondo, kanye nokufundiswa kokuphepha kokuphepha, ngoba kunzima kakhulu - ukuhlala Isifo esinjalo. Kunzima ingane ukuchaza ukuthi kungani engakwazi ukugijima nokudlala njengontanga yakhe, ngaphezu kwalokho, othisha ezinkulisa, othisha ezikoleni nabo bonke odokotela kudingeka baxwayise njalo ngempilo yengane. Noma kunjalo, nge ukwelashwa okufika ngesikhathi nangendlela efanele, iziguli ezine-hemophilia zihlala isikhathi eside njengabanye abantu.

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