EzempiloIzifo Nezimo

Isifo se-Kawasaki

Isifo se-Kawasaki asivamile, ikakhulukazi ezweni lakithi. Igama layo lingu-giant cell arteritis. Ngesikhathi sokuqala icala lichazwe ngo-1967, eJapane, lapho lesi sifo sisavame kakhulu kunakwamanye amazwe.

I-etiology yakhe ayitholakali ngokugcwele kodwa, ngokusho kokucabanga, i-agent causative yi-retrovirus, eholela ekuvuvukeni kwemithambo yegazi emzimbeni womuntu. Kuyathakazelisa ukuthi isifo sikaKawasaki sithinta ikakhulu izingane ezingaphansi kweminyaka engama-4, eziye zahluleka ukuzivikela, futhi kaningi abafana. Ezweni lakithi, ukutholakala ngokuthi "isifo se-Kawasaki" kuyinto engavamile kakhulu, amacala angaba ngu-10 ngonyaka. Kodwa-ke, isibalo sangempela singaba sikhulu, ngoba akuwona wonke udokotela okwazi ukubona izimpawu zesifo futhi ahlinzekwe kahle.

Naphezu kwezimpawu ezihlukahlukene, amaphuzu amaningana ayisihluthulelo abalulekile ukuze ahlolwe. Isifo se-Kawasaki siqala ngokunyuka kwamazinga okushisa, okungahlala ku-5-10 kuya ku-15-20days. Iziguli zihlakulela i-conjunctivitis, ezithinta kokubili amehlo. Ngemva kwamasonto amabili ukuqala kwalesi sifo, isikhumba ezintendeni nasezinhlakeni siba denser, reddens futhi siqala ukucima. Kwenzeka ukuthi isifo sikaKawasaki sihambisane nokuqhuma ezinxenyeni ezihlukahlukene zomzimba, okuyi-polymorphic in nature. Ngemva kwesikhashana, ivuvuka, bese iphela. Uma ubheka emlonyeni womntwana ogulayo, ungathola okuthiwa "i-sitrobheli", ulimi oluvuvukile, olubomvu olukhanyayo kanye nokuba khona kwamathumbu amancane ezinsini, ingxenyeni yangaphakathi yamahlathi. Izindebe zibuye zivuvuke futhi ziqhekeke. Ithuthukisa ama-hyperemia emphinjeni, ukucinana kwemisipha kubonakala. Ngokuvamile, ngakolunye uhlangothi entanyeni, ama-lymph nodes akhula, okuthi, lapho ephahlazeka, abangela ubuhlungu. Izimpawu ezihambisana nalesi sifo i-Kawasaki zibandakanya ikhanda, i-malaise ejwayelekile, ubuhlungu obuhlangene, isisu esidabukisayo ehambisana nosizi nokuhlanza.

Ukuxilongwa kwenziwa ngudokotela kokubili ngesisekelo sezimpawu zomtholampilo, futhi kuqondiswa imiphumela yokuhlaziya kwesiguli. Uma igazi leguli liphakeme amazinga e-ESR, amaprotheni asebenzayo e-C, antitrypsin, transaminase, kanye nezinkomba zikhuluma nge-anemia kanye ne-thrombocytosis, kanti udokotela ngeke akungabazeki ukuxilongwa kwe-Kawasaki. Lesi sifo sibonakala nokuba khona emceni wamaprotheni kanye ne-pus.

Lesi sifo sinengozi ngoba singabangela izinkinga enhliziyweni, kuze kube khona ukuhluleka kwenhliziyo, ukuhlukunyezwa kwe-myocardial kanye ne- jaundice yomshini. Isiguli ngesisulu esincane se-Kawasaki sithunyelwa ukubonwa ku-cardiologist kanye ne-echocardiography. Ngendlela elula yesifo, ukuvuvukala kwemisipha yenhliziyo kwenzeka. Nakuba izibalo ezimweni ezinjalo zingavamile. Kodwa i-aneurysm ye- coronary arteries ngokuvamile ivela kuma-20% weziguli. Uma, ngesikhathi sokugula, izibilini zobuchopho zithinteka, khona-ke i-aseptic meningitis ingakhula. Njengoba izimbangela ze-arthritis zibonakala, ukubandakanyeka kwe-gallbladder-dropsy, kanye ne-otitis media kusebenza nasezinkingeni.

Lapho ukwelapha lesi sifo, okokuqala, kugxila ekuqinisekiseni ukuvikelwa kwesimiso senhliziyo nokuvimbela ukwehluleka komsebenzi wayo. Isiguli sigunyazwe izidakamizwa ezingekho-steroidal anti-inflammatory ngamazinga aphezulu, ama-cretic corticosteroid namafutha. Nsuku zonke ngezinsuku ezingu-5-7 isiguli sijova nge-immunoglobulin nge-intravenously, ukuthuthukisa ingculazi nokuphumula okusheshayo kwesiguli. Umuthi onjalo owaziwayo njenge-aspirin, uyakwazi ukunikeza usizo olubalulekile ekulwa nesifo esingavamile. Ihlanganisa izakhiwo eziningana ngesikhathi esisodwa futhi isetshenziswe njenge-antipyretic, anti-inflammatory and blood thinning remedy. Endabeni ye-Kawasaki isifo, sisetshenziselwa ngisho nabantwana abangaphansi kweminyaka engu-12 ubudala. Muva nje, ukuxoshwa kwegazi, iziguli zichazwe i-heparin. Ngokuphumelela ngokukhethekile, isifo sikaKawasaki siphathwa ezindaweni zokwelapha zika-Israyeli, lapho iziguli zihamba khona ngenqubo ye-plasmapheresis - ukuhlanzwa kwe-plasma yegazi.

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