ImpiloIzifo nemibandela

I anomaly Arnold Chiari

Anomaly Arnold Chiari ephelezelwa dystopia (ukwephulwa indawo) izakhiwo ku posterior fossa cranial offset kubo ngokusebenzisa enkulu wazalela entanyeni ngaphandle kogebhezi ku umsele umgogodla. Ukushenxisa amalaka cerebellar noma ingxenye ngase engxenyeni engenhla umsele vertebral.

Kunezinhlobo ezine yalesi sifo. Anomaly Arnold Chiari Uhlobo 1 kuboniswa offset amalaka cerebellar, hhayi ephelezelwa ezengeziwe ukuthuthukiswa anomalies ingqondo. Lolu hlobo kubonakala abantu ngemva engamashumi amathathu. Eyesibili uhlobo ukwephulwa izindawo izakhiwo ku fossa posterior futhi amalaka cerebellar. Ngokuvamile lolu hlobo sitholakale izingane. Uhlobo lwesithathu yezindawo anomaly zihlanganisa ukwephula cishe zonke izakhiwo e fossa zadnecherepnoy. Ukubonakaliswa lolu hlobo lokusebenza aluhambisani ne ukuphila. Uhlobo lwesine anomaly inikeze kubhekwe ukushintshashintsha nokungathuthuki we cerebellum. neurosurgery Modern uyalandisa yona Dandy-Walker syndrome.

Ngo-indentation cerebellum engxenyeni engenhla umsele umgogodla kuyinto ukuphazamiseka evamile outflow oludakayo ukuthi ivikela asebuchosheni nomgogodla. Ukukhubazeka e CSF kwegazi kungabangela ukuvaleka amasignali ngobulili kusukela ingqondo nezitho noma ukuqongelela cerebrospinal fluid. Ingcindezi ukuthi cerebellum ine phezu emgogodleni kungaholela syringomyelia.

Ngokusho kochwepheshe abaningi, u-Arnold Chiari anomaly ubhekwa kuyisifo esiwufuzo. Nokho, kufanele kuphawulwe ukuthi izifundo okuhloswe ngaso aphenya lokhu isici, kukhona lapho besanda kuqala.

Iziguli eziningi ukuphathwa yilesi sifo, it is hhayi waphawula nezimpawu noma izimpawu zesifo. Iziguli ezinjalo ukuthola akukho ukwelashwa. Ukuthola yesifo kwenzeka kuphela sitholakele nezinye izifo.

Ukuthuthukiswa lesi sifo ezimweni eziningi ephelezelwa ikhanda, sokucasuka ukukhwehlela, sneezing noma ukuzikhandla ngokweqile ngokomzimba, ukuba ndikindiki futhi ukunsonsotha kwezandla, ayephuli lokushisa-sensitive futhi ngenxa yalokho, ukusha njalo. Ngaphezu kwalokho, isifo libhekene ubuhlungu wesibeletho esifundeni noma wesibeletho, ngezikhathi ezitshekile emahlombe. Ziningi izithiyo e ekulondolozeni ukulinganisela (Gait engalingani) kanye buthakathaka kusebentisana isandla.

Ngoba eziningi izimpawu zesifo ivame ukuhlotshaniswa nezinye izifo, kubalulekile ukuthola uphethwe ephelele.

izinyathelo Yokucwaninga uqale nge luhlolo nenhlolovo nesineke. Uma isiguli ekhononda zobuhlungu ekhanda, kodwa isizathu nesenzakalo yabo Akucaci kumuntu onekhono, kuyothiwa babelwe MRI. Ukuxilonga ivumela ngokwanele ukubone ngokuthe ngqo khona isifo.

Kwezinye izimo, u-Arnold Chiari anomaly iba isifo eqhubekayo kuholela eziyingozi kakhulu. Lezi zihlanganisa iphimbo (uketshezi olunqwabelene ebuchosheni). Ngakho kunesidingo ngamapayipi nezimo for uzotshala i-cerebrospinal fluid kwenye indawo emzimbeni. Izinkinga lesi sifo futhi zihlanganisa ukukhubazeka. Kutfutfukisa ngenxa yokucinana umgogodla. Syringomyelia uyalandisa futhi nezinkinga kungenzeka. It kuhambisana kumiswa izinhlumba kabuhlungu emgogodleni noma umgodi, okuyinto ugcwele cerebrospinal fluid kanye kunikeza umsebenzi.

Iziguli abe Arnold-Chiari ukwelashwa kwakuphambene nemvelo unikezwa ngokuhambisana kobukhulu isimo. In the ukungabikho izimpawu, ngokuvamile aqokwe zokuqapha njalo futhi ukuhlolwa. Lapho ukubonakaliswa izimpawu udokotela oyinhloko angabeka amaphilisi ezinhlungu. Nokho, iningi ekwelapheni lesi sifo kwenziwa surgically.

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