Lennox-Gastaut syndrome (isithuthwane)

Lennox-Gastaut syndrome - uhlobo isithuthwane (myoclonic-astatic). Ezinjalo izifo samuntu kuhilela inhlanganisela tonic nokuquleka atonic, atypical ukungabi sokuwa imisiwe kwengqondo in izinsana. Ngokokuqala ngqá sifo ukuzibonakalisa ezinganeni kusukela zi oyedwa kuya kwabahlanu, ikakhulukazi abafana.

Lesi sifo ngokuvamile eba ngenxa idluliselwe ebuntwaneni izifo zezinzwa futhi iqala ukwehla kwamamaki okungalindelekile emsebenzini ingane. Ngemva kwesikhathi esithile, kukhona Ukudlikizela, ukuquleka, baveze kwengqondo kancane, futhi intelligence encishisiwe.

Kancane kancane, ngosizo ukukhula komntwana, ubunjalo nokuquleka kuyahlukahluka. Fall sithathelwe indawo ngokwengxenye, okwesibili generalized, ukuhlaselwa eyinkimbinkimbi isithuthwane.

Ngenxa yalokho kuboniswa Lennox-Gastaut syndrome

Ukuze uqonde izimbangela yilesi sifo kunzima ngokwanele, kodwa kuze kube manje eyaziwa yibo main.

• I anomaly we kobuchopho.
• ngamagciwane okunzima (meningitis, encephalitis, rubella).
• nezifo ngenxa yezakhi zofuzo sokugembula ubuchopho (CNS, izifo umzimba, ukuqina kwamathishu tuberculous).
• ingane balimala ukudlula emgudwini wokuzala (lokuzalwa asphyxia, wazalwa kungakabi isikhathi, njll).
• CNS ukulimala kwesikhathi perinatal, kanye preterm ukulethwa futhi asphyxia.

Izimpawu ze-PLGA

Lennox-Gastaut syndrome kungenziwa obonwa uphawu ezibaluleke kakhulu - I-nokuquleka. Izingane uxilongwe "isithuthwane idiopathic" libuye likhulume ngokuzila amafomu ahlukahlukene of isithuthwane (izimpawu) :

• paroxysms ukuwa;
• ukuquleka atonic;
• usuke ungekho atypical;
• ukuquleka esinqunyiwe;
• amajaqamba sternocleidomastoid;
• ukuquleka myoclonic-astatic;
• ukuquleka tonic (ngokuvamile kwenzeka phakathi ubuthongo obukhulu);
• TC generalized nokuquleka.

Iziguli sifo ka Lennox-Gastaut futhi abe nesimo sobuntu stupor nge inguquko bushelelezi e yisithuthwane ngokulandelana kwawo, retardation engqondo, engqondweni yethu neziyaluyalu ubuntu.

Ukuhlonza Ukugula syndrome LH

Ngokushesha ngemva izimpawu zokuqala zesifo kumele ngokushesha bafune usizo lobuchwepheshe, shayela i-ambulense. Ngokuvamile, sitholakele isifo Kwenziwa usebenzisa ECG phakathi nokuhlasela.

LH Syndrome Ukwelashwa

Lennox-Gastaut sifo ngemithi namasu kuhlinzwa. Ukwelashwa ngemithi ukuba nemiphumela emihle e akukho kuka-20% amacala. Esikhathini kuhlinzwa ukwelashwa indlela ekuqedeni amathonsi okungazelelwe, kuyaphumelela ukusika callosum Corpus (callosotomy). Futhi, ukusebenza ukusetshenziswa iqondiswe ukukhuthazwa emsipheni vagus nokususwa izimila semithambo kanye kombungu.

Nokho, kufanele kuphawulwe ukuthi ukuquleka nobuntu yilesi sifo ngokuvamile kunzima ukuyelapha; ekugcineni zingase zibangele isiguli nemiphumela enqala zenhlalo nezengqondo. ukuquleka tonic Cishe untreatable, okuyizinto ezibangela wehlise biko.