West syndrome

Ngokokuqala ngqá ongaziwa zibe kwezinsana iye yachazwa ngo West 1841st. Khona-ke kwaba umbuzo indodana yakhe siqu. Ikakhulukazi kugcizelelwe ngokuqhubekayo ethuthuka izimpawu lengqondo e. Lesi sifo aselapheki.

West syndrome kufakwe izimpawu triad isici - uchungechunge ukuphindaphinda zibe, lengqondo retardation, izinguquko express (paroxysmal) ku Bheka. Qala kancane kancane, izimpawu zokuqala kungenzeka kahle ngisho izingane enempilo ngaphambili, nakuba ngokuvamile kubonakala ngokumelene isizinda ezinzima lengqondo ukubambezeleka. Kwande izingane kwezinyanga ezine kuya kweziyisithupha, kodwa kungenzeka Ngokuhamba kwesikhathi lesi sifo (kufika ku iminyaka emine). Boys obala isifo ngaphezulu.

zibe kwezinsana ngokuvamile ziyalingana, zamazwe amabili, dlala, nge ukusikwa ngokuzumayo amaqembu kwemisipha. ukuhlaselwa uhlamvu incike amaqembu abahilelekile (flexor, extensor). Amajaqamba kungenziwa ukusakaza noma kuwo wonke imisipha noma ngabanye (Imisipha yentamo, imisipha esiswini). Ngokuvamile atholakala zibe okuxubile, kulandele nokudlanga - flexor, ngisho lingandile - the extensor. Ngaphezu kwalokho, kukhona spasm incike isikhundla esithile somzimba.

West syndrome ngokuvamile ukuqaphela zibe ngokunembile flexor. Uma abathintekayo besisu imisipha-flexors, umzimba ungahlukaniswa ngokuvamile ube eligoqiwe ngesigamu. Lapho bazibandakanye emkhawulweni engenhla, ukunyakaza esandleni kuyenziwa umdlalo-ningenisa (kubonakala sengathi ingane yena kuqala ukuba bamukele). Nge ukubandakanywa imisipha flexor entanyeni esifanelana like nodding. Uma imisipha bazibandakanye ka kwebhande ehlombe, ingane njengoba shrugs. Zibe kungakhawulela nistagmoidnymi ukunyakaza noma jerking we inhlamvu yeso. ukwehluleka okungenzeka futhi zokuphefumula. Lesi yisihloko sokuqala izimpawu of isithuthwane.

Uhlobo zibe of etiology akuxhomekile, njengoba ayivumeli ukubikezela ukuthuthukiswa lesi sifo. Nokho, indima eyadlalwa khona wesimethri (asymmetry kubonisa lesion cortical). zibe Asymmetric zinqunywa, isibonelo, amehlo lateral-lead noma ikhanda.

Zibe zivamise ukwenzeka phezu ovukayo noma falling umntwana elele. Ngaphansi therebetween ngomzuzu isikhawu. Sizonyuka umfutho ke incipha. imvamisa ezahlukene - ukusuka zibe elilodwa emakhulwini ngosuku. Abakwazi kubangelwe kumdumo noma ethintekayo.

Sengibuyele isikhathi amajaqamba encishisiwe reactivity. Izingane osevele hamba, ezingenzeka ngokuzumayo iwe (ukuhlaselwa iconsi).

West syndrome ubhekwa uhlobo ezivame kakhulu encephalopathy nabanesithuthwane, okuholela nawokuphazamiseka kokusebenza kwengqondo. On zokuvimbela Ayikho idatha.

West syndrome kwenzeka ngenxa yezizathu ezihlukahlukene. Asphyxia - okuvame kakhulu. Ngaphezu kwalokho, kungaba angahlangani azalwa naso zobuchopho, ukopha intracranial, kanjalonjalo. Ngezinye izikhathi imbangela isifo ayikwazi ukucaciswa.

Uma ingane yakho ine West syndrome, impatho iqala ngokushesha. Ungase ukhethe yokwelapha wezokwelapha, futhi kungenzeka ukuthi kokungenela iyadingeka, futhi odokotela abahlinzayo ngubani ukususa isikhungo sokugembula, etholakala endaweni ethile ebuchosheni. Maye, ithuba ukuthola lesi sikhungo akusho ngaso sonke isikhathi kwenzeke, futhi kwezinye izimo, ngisho nalapho itholiwe, akunakwenzeka ukususa.

Uma imithi edingekayo ukuze kudlule Yiqiniso wamukela, ngamunye akhethiwe izidakamizwa ezikhethekile antiepileptic. Ukumisa nokuquleka kuyofakazela ukuba impumelelo ukwelashwa, Nokho, ukwelashwa kufanele kudluliselwe nakulabo nanhlanu (kanye nesibalo esiphansi) izinyanga. isipiliyoni Clinical uphakamisa ukuthethelelwa esitebeleni lesi sifo-60% izingane, ukuhlaselwa ezisele, ngeshwa, zivuselelwa.

odokotela Israeli uthi, izifo kanye cryptogenic ifomu Izibikezelo kungcono kakhulu. Fundzisisa ukunakekelwa shot ukuhlaselwa, ingane "outgrow" syndrome, ukubambezeleka zentuthuko is kushintshwe imidlalo zemfundo. Lapho ifomu siyefana Izibikezelo sibi kakhulu. Uma silawula ukudonsa off ukuhlaselwa nekugwema umthombo ukuqala isifo (malformation, izimila, izinhlumba), ukuchibiyela kangakanani izingqinamba kutintfo.