ImpiloIzifo nemibandela

Myelodysplastic syndrome

Myelodysplastic syndrome - iqembu lonke kuqhathaniswa izifo ezingavamile okuhlotshaniswa kahle umnkantsha. Umsebenzi oyinhloko umnkantsha - ukuthuthukiswa kwamangqamuzana egazi. Lesi sifo lihlotshaniswa kahle noma baveze eyodwa noma ngaphezulu izinhlobo zamangqamuzana egazi - kwamangqamuzana abomvu engeziwe, izinhlayiya zegazi noma leukocyte.

Ngenxa yokwehluleka enjalo ivele kwegazi, buthaka kwesimiso somzimba sokuzivikela ezifweni futhi igazi ekunqandeni, okubangela ukopha okukhulu. Myelodysplastic syndrome kungaba eyinhloko futhi ikhule ngaphandle kokuhlela kusengaphambili, ngaphandle kwesizathu. Uma sisheshe satholakala nokuningi ezinzima - lesibili, okuyinto zibangelwa kakhulu ngokuzishisa ngemisebe, usebenzisa ama-ejenti amakhemikhali nolaka, njll Kufanele kuqashelwe ukuthi ngokuvamile kakhulu syndrome myelodysplastic esiholela wegazi.

Lesi sifo ezivamile ngomshini engu-60, okungenani phakathi nezigaba sabantu - intsha, futhi akuvamile ezinganeni.

syndrome Myelodysplastic: izimpawu. isifo enjalo ezikhathini eziningi okwenzeka ezifihliwe futhi wathola ngengozi ngesikhathi luhlolo noma ukwelapha ezinye izifo.

Noma kunjalo, izimpawu yalesi sifo elihlobene ne yi yokuphazamiseka umnkantsha. Uma kwesilinganiso noma ikhwalithi kwamangqamuzana egazi abomvu incipha egazini - kukhona ukuntuleka kwegazi emzimbeni, okuyinto kuhambisana ukukhathala, ubuthakathaka, ukozela, iphika, isiyezi. Nge lemali obanele of leukocyte kakhulu ukuba zimbi kakhulu ukuzivikela komzimba - umzimba awukwazi ukubhekana ngisho ukutheleleka elula. Uma ukwephula ka platelet Ukwakheka kokuba thrombosis noma ukopha njalo, okuyinto okunzima ukuba ayeke.

Ngaphezu kwalokho, iziguli zingase esekhala ubuhlungu, kwemisipha izinhlungu zibe, abukhali kwesisindo, imfiva njalo.

Myelodysplastic syndrome izindlela zokuxilonga. Ukuze wafaka le uphethwe wokugcina, udokotela udinga imiphumela yokuhlolwa futhi izifundo nesineke. Ukuze uqale, enze ukuhlolwa egcwele igazi ukunquma inani kanye isilinganiso kwamangqamuzana egazi.

Isiguli ezinqunyiwe isifundo wethambo izicubu zobuchopho. Kuze kube yimanje, biopsy, lapho ukucubungula impahla eyatholakala ukuze uthole isifundo futhi ukukhomba thuthuva. Izintambo futhi uphethwe morphological impahla - kukuvumela ukuba ichaze indlela lesi sifo futhi isigaba saso yentuthuko.

Futhi kwakudingeka kanye nokuhlaziywa cytogenetic legazi, phakathi kwesikhathi lapho ungakwazi ukunquma ukuthi ingabe izinguquko eziyisisekelo zofuzo - lokhu kuyisihluthulelo ithole ukuxilongwa okufanele.

syndrome Myelodysplastic: ukwelashwa. Kukhethwa ukwelashwa incike ukuma isigaba lesi sifo, futhi engu-isiguli khona izifo concomitant. Ezimweni omnene esetshenziswa nge amazinga okukhishwa eliphansi izingxenye ngamakhemikhali. Ngezinye izikhathi olukhonjiswa njengedifolthi ethola ejenti immunomodulatory. Uma ukwephula ka platelet ukumpontshelwa wokuqamba asetshenziswe njengoba isilinganiso yesikhashana.

Kwezinye izimo, lo kuphela kungenzeka ikhambi - a umnkantsha ukufakelwa noma ekunqandeni iseli isingeniso. Lena cishe ukuphathwa kuphela elingakwazi sifinyelele eside ngcono umzimba. Ngeshwa, imisebenzi enjalo kuphela kungenzeka uma kuhlinzwa iziguli ezifuna uneminyaka engaphansi kwengu-60 ubudala, futhi, njengoba sekushiwo, eneminyaka engaba ngu-lezi zifo uxilongwe njalo kunabo.

syndrome Myelodysplastic: sezulu singaba njani. A udaba oluhlobene kwakunzima ukunikeza impendulo ecacile, ngoba kubalulekile ukucabangela esimweni ngasinye eceleni isifo. Impumelelo ukwelashwa incike yobudala lesiguli, uhlobo lesi sifo nezinye umehluko wemisindo nemiqondo yamagama amaningi.

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