ImpiloIzifo nemibandela

Rossolimo-Melkersson-Rosenthal syndrome: Izimpawu, Ukwelashwa

Melkersson-Rosenthal syndrome It ngokuthi isifo esingelapheki, ne triad izimpawu eziyinhloko. I zokugula kwegama kukhona amagama amabili odokotela. Melkersson echazwe izimpawu ezimbili, kwathi owesithathu imakwe Rosenthal. Ngenxa yalokho, lesi sifo Lethiwa odokotela ababili.

On Melkersson-Rosenthal syndrome

syndrome polyetiological. Lokubaluleke kakhulu ekuthuthukiseni yayo has eziningi izici:

  • njengemithi yokungezwani komzimba nokuthile samafayela;
  • vasomotor iziyaluyalu kanye nezici ezithile lezinceku kubo;
  • zokugula kohlelo lymph endaweni ikhanda nentamo;
  • foci ezingamahlalakhona ukutheleleka odontogenic;
  • sinusitis.

Ephambi kwezinduna Melkersson-Rosenthal syndrome kungenzeka Neuro-esiwohlozayo genesis yayo. Ukuvela lesi sifo zonyaka. Ikakhulu kusukela Melkersson-Rosenthal sifo sithinta abantu kuka-25 no-35 ubudala. Can liyochukuluza hypothermia isifo notshwala, kanye izinhlobo eziningi zezidakamizwa. Ukuzibandakanya Bilateral kuvamile - 75% kuzo zonke izimo. Kakhulu akuvamile - Emaceleni.

Izimpawu Melkersson-Rosenthal syndrome

Syndrome wabonakaliswa nokuvuvukala izindebe nezihlathi. Khona-ke iwohloka kancane kancane imisipha yobuso. Umuntu uba nzima unciphise amehlo, ukukhuluma, amakhona emlonyeni wathela uketshezi. Ngo amaphesenti angu-30 iziguli ziba emehlweni ezomile noma zamanzi. Zilinganiselwa ku-20% - sithuthukiswe bezibona imisindo ukuze kangangokuthi kuba edabukisayo. Yini enye elichaza Melkersson-Rosenthal izimpawu syndrome? Cishe 80% eziguli ngaphezu nokuvuvukala izindebe wazibona reddening yabo oluqinile, ulimi inyuka, ubuso bayo iba engalingani, esingemnandi. Isigamu iziguli ibhekene ubuhlungu bekhanda nokuquleka imiqulu.

Yini enye elinesimo zokugula?

Yiziphi izimpawu cerebral syndrome libhekene Rossolimo-Melkersson-Rosenthal? Ekuqaleni, kubalulekile ukusho ukuthi Rossolimo - yigama udokotela wesithathu, okwathi ngo 1901 wachaza makroheylit (izifo zomlomo, okwandisa usayizi yabo) lihambisana ebusweni emsipheni paresis. Kamuva wenza Melkersson. Kodwa kusukela izifo incazelo Rossolimo ngezinye izikhathi igama lakhe asetshenziswe zokugula isihloko.

syndrome Cerebral bambulwa ukuhlolisisa. It ungaboniswa njengoba:

  • ikhanda (migraine);
  • asymmetry ebusweni ;
  • ukukhubazeka ebusweni unyakazise imisipha yobuso ;
  • uphawu Bell lagophthalmos;
  • xerophthalmia;
  • hyperacusis;
  • dysarthria;
  • edema angioneurotic ebusweni (ngokuvamile izindebe);
  • ulimi fissured futhi macroglossia;
  • dizgevzii futhi ageusia;
  • cheilitis granulomatous.

Njengoba syndrome kwembulani?

Melkersson-Rosenthal syndrome, okuyinto inezithombe kulesi sihloko kungenziwa kunqunywa uphethwe. Kulokhu, labetibambile:

  • ukuhlolwa serological;
  • -X-ray, uma kukhona izinsolo ukuthi lesi sifo Kuvezwe ngenxa yezifo ezithathelwanayo (HIV, ugcunsula, isifo saseLyme, sarcoidosis);
  • electromyography;
  • Magnetic resonance imaging zobuchopho;
  • luhlolo peripheral.

Yiqiniso

Kangakanani isifo Melkersson-Rosenthal? Lesi sifo iqala ukuvuvukala ngaphansi kwesikhumba. It ke Ukhuthaza ukuba le mucosa ngomlomo. Khulisa ngobukhulu lip: phezulu - ngaphezulu ephansi - kancane. Ungezwa ubuhlungu we emsipheni ebusweni, futhi kamuva ukuthuthukisa ukukhubazeka.

Lesi sifo libhekene kuqala oyingozi. Ukuvuvukala eba amahora amaningana. Ngokuvamile kuba uhlelo olunzulu futhi ngokugcwele ithumba izindebe, okuyinto zipendwe okukhanyayo, tint ngezinye izikhathi bluish livela. Naseduzane komlomo ungakheka imifantu. inkulumo ephazamisekile, nobunzima ngokudla.

kuyinto esingamahlalakhona of Melkersson-Rosenthal kanjani? Lesi sifo futhi iqala ukuvuvukala. Kodwa-ke kuba njalo, kwandisa noma kuyancipha ngezinye izikhathi kuphela. Edema egcinwe zakhe ebusweni bonke kanye ngalo ingaphakathi ngomlomo.

It is a uhlobo ezingavamile Melkersson-Rosenthal syndrome, lapho izihlathi evuvukele kuphela. Ngokuvamile, lokhu kumane nje omunye wabo. On the kwangaphakathi ohlangothini izihlathi sihleli ngokucacile amazinyo. Lesi simo ubizwa ngokuthi "pair granulomatous." Ayikho izimpawu ukuvuvukala.

ukwelashwa

Kangakanani Melkersson-Rosenthal syndrome? Odokotela sebenzisa izindlela kuhlinzwa noma olandelanayo. Ekuqaleni, isiguli uphenywa ukuthola pathologies ukuthi lingase libangele isifo. ukwelashwa Steel akuvimbeli Ukuphinda futhi asetshenziswa kabanzi ngezinhloso ayeyisimonyo, lapho izicubu is excised izindebe.

Lapho ukwelashwa ngoludala imiphumela emihle kakhulu ingatholakala nge inhlanganisela corticosteroids, imithi elwa namagciwane kanye imithi olwa nomalaleveva. "Prednisolone" inikezwa ndawonye "Oxytetracycline". Sebenzisa pyrogenic kanye ejenti desensitizing. yokwelapha NJALO virus. Uma isiguli ozwelayo Staphylococcus ke osebenza "toxoid".

Sibekezele kokuba Melkersson-Rosenthal syndrome, okuphoqelekile multivitamins enqunyiwe, calcium pantothenate, nicotinic acid, vitamin A, abizwa ngokuthi "komplamin" Ukuze ngcono kwegazi emzimbeni esithambile. ukusetshenziswa Yiqiniso - izinsuku ezingu-10. A esimisiwe kahle "Cavintonum", "Tanakan" futhi "stugeron" athathwe 1 2 izinyanga. Iziguli kukhishelwa ngokuthi "Nerobolum". Lena izidakamizwa evimbela ukuguga. Amiswa njengamaphayona zinhlungu futhi sedatives.

Ukwelashwa ngokwezihloko

Yiziphi ezinye izindlela ingasetshenziswa unqobe sifo Melkersson-Rosenthal? Ukwelashwa kungaba nezokusigcoba. Ngesikhathi esifanayo wenza isicelo ka heparin wamafutha. Lapho zihlanganiswa nge Dimexidum, ushiya imizuzu 20. Inqubo wenziwa izikhathi 3 kuya 4 nsuku zonke. Inkambo - 3-4 amasonto.

Ukuze udebe lwangezansi isetshenziswa heparin elektrofarez. Inqubo wenziwa nsuku zonke. Lapho esetshenziswa imisinga fizlechenii Bernard, laser helium-neon kanye ultrasound.

Isicelo ngama-corticosteroid futhi methyluracyl yokugcoba asetshenziswa izinqubo ukuvuvukala. isifonyo sisetshenziswa imizuzu engu-20, izikhathi ezingu-2 kuya ku-3 nsuku zonke. Ngaphezu kwalokho, izicelo zenziwa kusukela izimali keratoplasty.

Sebenzisa ukuvinjelwa (3-4 ml), efudumele amaphesenti amabili-lidocaine, novocaine futhi trimecaine. Imijovo zenziwa nsuku zonke noma masonto kwezinsuku ezimbili.

Imiphumela Melkersson-Rosenthal syndrome

Syndrome ngokushesha kuba amahlala khona. Lokhu kuhlanganiswa khulu kubonakala e ukubukeka komuntu, okuyinto siphazamisekile futhi ekhubazekile ukuvuvukala. Ngenxa yalokhu ngokuvamile unesifo sokudangala nokuphazamiseka engqondweni. Ngenxa baxhashazwe okwandisiwe izindebe futhi indoda kanzima ukuhlafuna nokugwinya, inkulumo ukuhlanekezela siyenzeka. Ayangena evelayo lapho ukuvuvukala kanye singenzeka amagciwane ayingozi okubangela izifo ezithathelwanayo. Lokhu kusebenza futhi ulimi. Ngezinye izikhathi embozwe ukuqhekeka. Ngaphezu kwalokho, lokhu ingozi uyanda ngenxa yokulimala edematous mucosa amazinyo, isibonelo, phakathi ukuhlafuna ukudla.

Abantu abaphethwe yilesi sifo, kutuswa ukuba ukudla okuqinile ngaphezulu: izifundo zokuqala, ezihlukahlukene okusanhlamvu kanye nemikhiqizo yobisi. Lena kulula ukuhlafuna ukudla kunciphisa amathuba ekulimazeni mucosa ngomlomo. Izithelo nemifino nazo ewusizo, kodwa kudingeka ahlukaniswe tincetu encane bese wengeza ukuba salads. nezixhobo ezinkulu noma yikuphi ukudla okuthola kungcono ukuba ugaye e ukusetshenziswa Cutlery ukudla.

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