ImpiloIzifo nemibandela

Hypertelorism - Iyini? Izimbangela zesifo

Hypertelorism - igama, by okuyinto kwakusho zokugula libhekene ukwanda ngokweqile e ibanga phakathi kwezitho ezimbili abhanqiwe. Ezimweni eziningi kutholakala ukuthi uphethwe yini hypertelorism ocular, kodwa ezinye izinguquko sokugembula zokwelapha zamanje. Yilokhu esikubiza ukuchaza kamuva kulesi sihloko.

Hypertelorism - Iyini?

Leli gama akuve kuvamile ukuba amarekhodi yezokwelapha. Hypertelorism - okungukuthi, njengoba sekushiwo, a zokugula okuyinto kuhambisana nokwanda ibanga phakathi kwezitho ezimbili abhanqiwe. Kumele kuqashelwe ukuthi le ncazelo zaqala ukusetshenziswa akunjalo kudala - okokuqala e izincwadi ezisemthethweni, kwabonakala ngo-1924.

Ngokwesibonelo, imithi eyaziwa njengendlela zokugula enjalo hypertelorism izingono. Kulokhu, ukunikezwa kwe-okuthiwa embeleni Inkomba - Inkomba, okuyinto kunqunywa lihlela isilinganiso phakathi kwama selilonke kwesifuba ezingeni ingono futhi ibanga elibahlukanisile. Pathology akuyona ezimele futhi ngokuvamile eba ku isizinda kombungu esizalweni, ezifana Apert syndrome, isifo Edwards.

Kodwa lo esivame kakhulu esemkhathini hypertelorism - isifo lapho kukhona Ukwanda okungavamile ibanga phakathi nezinyawo iso. isimo esinjalo kokuzalwa - ke ukuthi unesifo ezinsukwini zakuqala emva kokuzalwa.

Ziyini izimbangela zezifo

Hypertelorism iso - disorder azalwa naso, okuyinto ngokujwayelekile ohambisana nesifanekiso ezahlukene nezifo ngenxa yezakhi zofuzo. Ngokwesibonelo, futhi kabanzi esilinganayo iso enethiwekhi kuyagcinwa nezingane nefrofibromatozom, Apert syndrome, i-Down Syndrome, Toast, Edwards nezinye izifo ukuthi ahambisana kombungu amaningi we-fetus. Ngezizathu ezifanayo ngqo zihlanganisa kwezinso ezahlukene isakhiwo ubuchopho noma ikhanda - kuba phambi izimila, ukuphulukisa lishesha kakhulu zezitho Yekhanda, kuhlasimulise ubuchopho herniation nemifantu.

Yiqiniso, kungenzeka ukuba sibone ezinye futhi izici eziyingozi ukuthi zingaphazamisa evamile ukuthuthukiswa kokubeletha , noma ucuphe atholakale kwezinso fetus zofuzo. Ngakho, nomthelela omubi isimo somntwana ehlaselwe ukutheleleka idluliselwe by umama ngesikhathi sokukhulelwa, kanye engena emzimbeni ubuthi, kuhlanganise nezidakamizwa esindayo, ebulilini utshwala, izidakamizwa nokunye. D.

Hypertelorism: isithombe kanye ezihambisana nezimpawu

Kuthiwa hypertelorism has degree ezahlukene - ezinye iziguli iso kancane kuphela dengwane, kuyilapho abanye zingabantu ububanzi ngaphandle nodokotela wakho ungase uphawule isici emva ukubukeka lokuqala ngesikhathi umntwana. Lezi zingane abe izici isici kakhulu ebusweni babo isakhiwo:

  • ibanga pathologically ezinkulu phakathi ubuso engaphakathi enethiwekhi.
  • Ngokuvamile ukusonteka palpebral emifantwini ukubonwa - sebenayo ukuma okungajwayelekile, noma kube azilingani ayisesemikhulu kakhulu.
  • Kukhona isakhiwo sici ekhaleni - emuva zakhe uyisicaba naseduze ekhaleni ibhuloho.
  • Ngokuvamile nge hypertelorism e abanezingane okwatholakala strabismus, ezihlukahlukene of ongaboni lo ukusonteka of emsipheni optic, ukuba inkinga nephunga.

Ngeshwa, izimpawu ngenhla zofuzo isici hhayi kuphela ukuhlukumeza isakhiwo phambi ugebhezi. Ngokuvamile, izingane kufanele unyawo sengozini, ukuthuthukiswa okungavamile isiphanga nemihlathi kahle ekukhuleni.

izindlela zokuxilonga

Yiqiniso, kulesi simo, kubaluleke kakhulu ukuxilonga kahle, ngoba udinga ukucacisa khona isifo esithile zofuzo. Doctor sinquma le interorbit okruzhnostnoy-index, okuyinto kunqunywa sokuhlukanisa kulinganiswa ikhanda selilonke ibanga phakathi emakhoneni engaphakathi amehlo izimbotshana, futhi nenombolo okuholela iyanda yi 100. zokugula ngokuvamile kusho esimweni lapho Inkomba idlula 6.8 .

Ngaphezu kwalokho olwenziwa abazali anamnesis futhi ukucwaninga ngofuzo. Futhi, qiniseka ukuthi ingane yakho ebekiwe resonance kazibuthe noma computed tomography ikhanda - le nqubo kungathola ithambo kwezinso futhi khona izimila ebuchosheni.

ukuphathwa isifo

Uma sikhuluma hypertelorism ke oluthile lokwelapha liyadingeka kuphela uma kwenzeka ukuthi kukhona usongo olukhulu izinhlaka umbono kanye kwalapho kuhlangana khona imizwa. Kulokhu kutuswa ukuhlinzwa. Ngesikhathi inqubo, udokotela wenza skull plastic. Kodwa-ke, isinqumo ukubamba ukusebenza kudinga onguchwepheshe, benaka ezicini eziningi, kuhlanganise isimo somntwana futhi khona comorbidities. Ukuhlinzwa ngokuvamile kwenziwa nangaphambi kokuba isiguli sibe iminyaka emibili ubudala - lesi yisikhathi ukusebenza unika imiphumela elilungile kakhulu.

Njengoba for ukwelashwa letindzala, siqondiswe ukulungiswa lesi sifo eyinhloko. Kule futhi kuncike yokwelapha wezokwelapha.

Ukuvimbela isifo kanye Izibikezelo iziguli

Hypertelorism - kunalokho, kuba isici yobuhle. Izingozi zihlanganisa syndromes nezifo okuyinto ahambisana nalesi sifo. Ngakho-ke, isici ngokwako akusona usongo ekuphileni komntwana. Okukhishwayo kuphela yilabo ezimweni lapho iso enethiwekhi ukonakala kuthinta umbono lesiguli.

Mayelana zokuvimbela, indlela ngeshwa ezithile ekuvimbeleni ptologii echazwe ayikho. Ukuze kuncishiswe ingozi izifo intrauterine, ngesikhathi sokukhulelwa kufanele ukuqapha ngokucophelela ezempilo, ukudla ngendlela efanele, ukuyeka ukubhema, utshwala, izidakamizwa kanye nezidakamizwa yingozi.

Ukuhlela ukukhulelwa futhi kufanele luphathwe ngendlela efanele hhayi ukulahla yokubonisana kuhlelwe nge isazi sezakhi zofuzo. Ezinye izifo zofuzo umuntu kungaba ihlonzwe ngisho utero. Ucwaningo zofuzo phakathi ukuhlela sokukhulelwa ukusiza ukuthola amathuba ingane ukuphambuka.

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